[{"@context":"https:\/\/schema.org\/","@type":"Article","@id":"https:\/\/www.nyon.cz\/zivot-s-fenylketonurii\/#Article","mainEntityOfPage":"https:\/\/www.nyon.cz\/zivot-s-fenylketonurii\/","headline":"\u017divot s fenylketonuri\u00ed","name":"\u017divot s fenylketonuri\u00ed","description":"\u017divoty a \u017eivotn\u00ed styly v\u0161ech lid\u00ed se velmi li\u0161\u00ed, proto\u017ee ne ka\u017ed\u00fd m\u00e1me stejn\u00e9 z\u00e1zem\u00ed, nap\u0159\u00edklad \u017eivotn\u00ed styl \u010dlov\u011bka bez...","datePublished":"2021-08-29","dateModified":"2021-08-29","author":{"@type":"Person","@id":"https:\/\/www.nyon.cz\/author\/#Person","name":"","url":"https:\/\/www.nyon.cz\/author\/","identifier":1,"image":{"@type":"ImageObject","@id":"https:\/\/secure.gravatar.com\/avatar\/69bd9b72104e3ccfb6214cbd23cb226f96c6ecf33a2a351fa1d4682235118df3?s=96&d=mm&r=g","url":"https:\/\/secure.gravatar.com\/avatar\/69bd9b72104e3ccfb6214cbd23cb226f96c6ecf33a2a351fa1d4682235118df3?s=96&d=mm&r=g","height":96,"width":96}},"publisher":{"@type":"Organization","name":"nyon.cz","logo":{"@type":"ImageObject","@id":"\/logo.png","url":"\/logo.png","width":600,"height":60}},"image":{"@type":"ImageObject","@id":"https:\/\/www.nyon.cz\/wp-content\/uploads\/salmon-ga6d34c947_640.jpg","url":"https:\/\/www.nyon.cz\/wp-content\/uploads\/salmon-ga6d34c947_640.jpg","height":0,"width":0},"url":"https:\/\/www.nyon.cz\/zivot-s-fenylketonurii\/","about":["\u017divotn\u00ed styl"],"wordCount":454,"articleBody":"\u017divoty a \u017eivotn\u00ed styly v\u0161ech lid\u00ed se velmi li\u0161\u00ed, proto\u017ee ne ka\u017ed\u00fd m\u00e1me stejn\u00e9 z\u00e1zem\u00ed, nap\u0159\u00edklad \u017eivotn\u00ed styl \u010dlov\u011bka bez st\u0159echy nad hlavou bude velmi odli\u0161n\u00fd \u017eivotn\u00edmu stylu n\u011bkoho, kdo m\u00e1 ide\u00e1ln\u00ed \u017eivot \u2013 rodinu, d\u016fm, zahr\u00e1dku, pejska,\u2026 Takov\u00fd \u017eivotn\u00ed styl by bral skoro ka\u017ed\u00fd, av\u0161ak takhle \u017eivot nefunguje a to v\u0161ichni na sv\u011bt\u011b v\u00edme. \u017divot je krut\u00fd, s\u00e1z\u00ed n\u00e1m p\u0159ek\u00e1\u017eky jednu za druhou a nen\u00ed to v\u016fbec jednoduch\u00e9. Ka\u017ed\u00fd m\u00e1 n\u011bjak\u00fd probl\u00e9m, a to i v\u00fd\u0161e zm\u00edn\u011bn\u00fd \u010dlov\u011bk, co m\u00e1 v\u0161e, co by si p\u0159\u00e1l, proto\u017ee rodina, bydlen\u00ed a pen\u00edze jsou v\u00a0dne\u0161n\u00ed dob\u011b v\u0161e, i tak ale m\u016f\u017eeme m\u00edt psychick\u00e9 probl\u00e9my a nejen to. \u017divot n\u00e1m m\u016f\u017ee nad\u011blit n\u011bco hor\u0161\u00edho, co se ned\u00e1 zm\u011bnit. R\u016fzn\u00e9 poruchy \u010di zdravotn\u00ed probl\u00e9my. A jeden z\u00a0nich, nebo respektive nemoc, je fenylketonurie. Jedn\u00e1 se o genetickou poruchu, kdy d\u00edky \u0161patn\u00e9 kombinace gen\u016f od rodi\u010d\u016f m\u016f\u017ee doj\u00edt k\u00a0chyb\u011b a t\u011blo neobsahuje enzym, kter\u00fd by dok\u00e1zal \u0161t\u011bpit b\u00edlkoviny, tud\u00ed\u017e t\u011blo b\u00edlkoviny nesm\u00ed p\u0159ij\u00edmat. Je to velmi zjednodu\u0161en\u00e1 verze, ale na takov\u00e9mto principu to pr\u00e1v\u011b funguje. Lid\u00e9 trp\u00edc\u00ed fenylketonuri\u00ed maj\u00ed velkou p\u0159ek\u00e1\u017eku v\u00a0\u017eivot\u011b, a to je dieta. Jeliko\u017e jejich t\u011blo nesm\u00ed p\u0159ijmout v\u011bt\u0161\u00ed mno\u017estv\u00ed b\u00edlkovin \u2013 zde z\u00e1le\u017e\u00ed na stupni t\u00e9to nemoci \u2013 mus\u00ed si hl\u00eddat, co za potraviny p\u0159ijmou. Nesm\u00ed to b\u00fdt potraviny s\u00a0b\u00edlkovinnou slo\u017ekou \u2013 maso, ml\u00e9ko, lu\u0161t\u011bniny, vaj\u00ed\u010dko a podobn\u011b. Ov\u0161em zde z\u00e1le\u017e\u00ed na tom, jak siln\u011b je touto nemoc\u00ed jedinec posti\u017een.N\u011bkte\u0159\u00ed nesm\u00ed ani hloup\u00e9 vaj\u00ed\u010dko, jin\u00ed si daj\u00ed t\u0159eba dv\u011b vaj\u00ed\u010dka na sn\u00eddani a jsou v\u00a0po\u0159\u00e1dku. To, kolik sm\u00ed a nesm\u00ed jim p\u0159esn\u011b \u0159ekne doktor. Tak\u00e9 tito lid\u00e9 mus\u00ed po\u017e\u00edvat pr\u00e1\u0161ek, d\u00edky kter\u00e9mu do t\u011bla d\u00e1vaj\u00ed podobn\u00e9 l\u00e1tky b\u00edlkovin\u00e1m, proto\u017ee t\u011blo tyto l\u00e1tky pot\u0159ebuje. Celkem s\u00edla, \u017ee?\u00a0Co se stane, pokud t\u011blo po\u017eije b\u00edlkovinu? Kdyby si dal lehk\u00fd fenylketonurik kole\u010dko klob\u00e1sy, tak se pozvrac\u00ed. Kdyby si dal ku\u0159ec\u00ed stehno, mohlo by doj\u00edt k\u00a0v\u00e1\u017en\u00e9mu po\u0161kozen\u00ed mozku, a to zejm\u00e9na u mlad\u0161\u00edch d\u011bt\u00ed, proto je velmi d\u016fle\u017eit\u00e9 zejm\u00e9na mlad\u0161\u00ed fenylketonuriky obrovsky hl\u00eddat. Po\u0161kozen\u00ed mozku by zap\u0159\u00ed\u010dinilo ochrnut\u00ed, demenci, apod.                                                                                                                                                                                                                                                                                                                                                                                         4\/5 - (3 votes)        "},{"@context":"https:\/\/schema.org\/","@type":"BreadcrumbList","itemListElement":[{"@type":"ListItem","position":1,"name":"\u017divot s fenylketonuri\u00ed","item":"https:\/\/www.nyon.cz\/zivot-s-fenylketonurii\/#breadcrumbitem"}]}]